Diagnóstico diferencial da mielofibrose (MF)1,2,3


Referências
1. Khoury JD, Solary E, Abla O, Akkari Y, Alaggio R, Apperley JF, et al. The 5th edition of the World Health Organization Classification of Haematolymphoid Tumours: Myeloid and Histiocytic/Dendritic Neoplasms. Leukemia. 2022 Jul;36(7):1703-19. 2. Arber DA, Orazi A, Hasserjian RP, Borowitz MJ, Calvo KR, Kvasnicka HM, et al. International Consensus Classification of Myeloid Neoplasms and Acute Leukemias: Integrating morphologic, clinical, and genomic data. Blood.2022 Sep 15;140(11):1200-28. 3. Valente ACMM, Ribeiro RT. Diagnóstico hematológico e molecular das neoplasias mieloproliferativas crônicas BCR-ABL negativas. RBAC. 2021;53(4):344-51 4. Mesa RA, Verstovsek S, Cervantes F, Barosi G, Reilly JT, Dupriez B, et al. International Working. Group for Myelofibrosis Research and Treatment (IWG-MRT). Primary myelofibrosis (PMF), post polycythemia vera myelofibrosis (post-PV MF), post essential thrombocythemia myelofibrosis (post-ET MF), blast phase PMF (PMF-BP): Consensus on terminology by the international working group for myelofibrosis research and treatment (IWG-MRT). Leuk Res. 2007 Jun;31(6):737-40. 5. McLornan DP, Godfrey AL, Green A, Frewin R, Arami S, Brady J, et al. BSH Committee. Diagnosis and evaluation of prognosis of myelofibrosis: A British Society for Haematology Guideline. Br J Haematol. 2024 Jan;204(1):127-35. 6. Tefferi A. Primary myelofibrosis: 2023 update on diagnosis, risk-stratification, and management. Am J Hematol. 2023 May;98(5):801-21 7. Chauffaille MLLF. Myeloproliferative neoplasms: a review of diagnostic criteria and clinical aspects. RBAC. 2010;32(4):308-16. 8. Barbui T, Thiele J, Gisslinger H, Kvasnicka HM, Vannucchi AM, Guglielmelli P, et al. The 2016 WHO classification and diagnostic criteria for myeloproliferative neoplasms: document summary and in-depth discussion. Blood Cancer J. 2018 Feb 9;8(2):15.JAKAVI®
ruxolitinibe
VIA ORAL
Clique para ler a bula de Jakavi® na íntegra.
Contraindicações: Jakavi® é contraindicado em pacientes com hipersensibilidade a ruxolitinibe ou a qualquer um dos excipientes.
Interações Medicamentosas: Deve-se ter cautela com inibidores de CYP3A4 e/ou inibidores duplos moderados das enzimas CYP2C9 e CYP3A4.
BR-33479